From a technical point of view we found appropriate the Society for Cardiovascular Magnetic Resonance (SCMR) recommendations, the Cardiovascular Magnetic Resonance (CMR) protocols for ARVD assessment must include left ventricle structure and function sequences, as well as transaxial or oblique transaxial SSFP cine images, with optional black blood images, fat suppression or late gadolinium enhancement sequences.

Major and Minor Cardiac MRI diagnostic criteria are quantifying the regional wall motion abnormalities (akinesia, dyskinesia or dyssynchronous RV), right ventricular dilatation and/or the reduced right ventricular ejection fraction.

Reasons to consider another test than CMR include the presence of contraindications to MRI, and severe renal failure (eGFR<30)(6).

According to the reporting guidelines (8) recommended by the Society for Cardiovascular Magnetic Resonance, to provide a framework for reporting results of cardiovascular magnetic resonance examinations, it is recommended that each report should identify the major and minor criteria associated with ARVC. 

Therefore a report should include information regarding:

1. Global right ventricular performance (RVEF);

2. RV dilation;

3. Location of Regional RV wall motion abnormalities (infundibulum, body or apex of right ventricle).

When acquired:

1. Fatty infiltration of the right ventricle, and

2. Occurrence of fibrosis by LGE should be provided.

Differential diagnosis considerations include:

•  pathologies causing RV volume overload, intracardiac shunts (e.g. atrial septal defects and anomalous pulmonary venous drainage),

• extracardiac shunts

•  cardiac displacement 

•  scarring conditions (sarcoidosis, myocarditis)

•  Uhl anomaly. (9,10)